Product ID: M2521
Stable red fluorogenic substrate for measurement of α-galactosidase activity, a lack of which is indicative of Fabry disease.
|Soluble In||DMSO, H2 O|
|Storage Conditions||Frozen, desiccated, protected from light|
- Kwapiszewskia R, Czartoryskab B, Ziolkowskaa K, Chudya M, Dybkoa A, Brzozkaa Z,"Substrate inhibition of lysosomal hydrolases: α-Galactosidase A and β-glucocerebrosidase." Clinical Biochemistry, 44: 941-943.
- Hoelzl MA, Gaertner M, Kovarik JJ, Hofer J, Bernheimer H, Sunder-Plassmann G, Zlabinger GJ (2010) "Quantification of α-galactosidase activity in intact leukocytes." Clinica Chimica Acta, 411: 1666-1670.
- Chamoles NA, Blanco M, Gaggioli D (2001) "Fabry disease: enzymatic diagnosis in dried blood spots on filter paper," Clinica Chimica Acta 308: 195-196.
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